Marfan syndrome is a multisystem connective tissue disorder, with primary involvement of the cardiovascular, ocular, and skeletal systems. Clinical diagnosis of Marfan syndrome has been based on the Ghent criteria since 1996. Among its many different clinical manifestations, cardiovascular involvement deserves special consideration, owing to its impact on prognosis. Pregnant women with Marfan syndrome are at a particularly high risk of adverse pregnancy and cardiovascular events. We e-mail you images of a case of a woman with Marfan syndrome and pregnancy who died at the postpartum period due to an aortic thoracic-abdominal aneurysm.